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Atrofia musculara spinala infantila (AMS tip I)cunoscuta si ca boala Werdnig-Hoffman,este caracterizeaza prin atrofii musculare si prin paralizii de origine spinala si apare de obicei in jurul varstei de 6 luni.
Semne si simptome:
-atrofii si paralizii la nivelul musculaturii spatelui
-atrofii si paralizii la nivelul membrelor inferioar
-disparitia reflexelor